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查看说明书Recombinant Human alpha-Galactosidase A / GLA Protein (His tag)
Cat#:TP07972应用：Positive Control; Immunogen; SDS-PAGE; WB
| Product Name: | Galactosidase alpha Recombinant Rabbit mAb |
| Cat No.: | RMA01814 |
| Clonality: | Monoclonal |
| Species Reactivity: | Human |
| Tested Applications: | WB,IHC,ICC/IF,FC,IP |
| Recommended Dilution: | WB,IHC,ICC/IF,FC,IP |
| Size: | 30ul 50ul 100uL |
| Format: | Liquid |
| Source: | Rabbit |
| Purification Method: | Affinity Purification |
| Isotype: | IgG |
| Conjugate: | Un-conjugated |
| Storage: | Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide a |
| Immunogen: | A synthetic peptide of human Galactosidase alpha |
| Calculated Molecular Weight: | 49 kDa |
| Observed Molecular Weight: | 49 kDa |
| GenBank Accession Number: | P06280 |
| Gene ID (NCBI): | 2717 |
| Synonyms: | GALA |
| Background: | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
| Category: | Primary Ab |
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