Recombinant Ornithine Transcarbamylase (OTC)
Cat#:TP03268应用:Positive Control; Immunogen; SDS-PAGE; WB
Product Name: | Ornithine Carbamoyltransferase Rabbit pAb |
Cat No.: | DPA01411 |
Clonality: | Polyclonal |
Species Reactivity: | Human, Mouse, Rat |
Tested Applications: | WB,IHC,IP |
Recommended Dilution: | WB: 1:1000 IHC: 1:20 IP: 1:20 |
Size: | 30ul 50ul 100uL |
Format: | Liquid |
Source: | Rabbit |
Purification Method: | Affinity Purification |
Isotype: | IgG |
Conjugate: | Un-conjugated |
Storage: | Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide a |
Immunogen: | A synthetic peptide of human Ornithine Carbamoyltransferase |
Calculated Molecular Weight: | 40 kDa |
Observed Molecular Weight: | 40 kDa |
GenBank Accession Number: | P00480 |
Gene ID (NCBI): | 5009 |
Synonyms: | OCTD |
Background: | This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008] |
Category: | Primary Ab |