Recombinant Hydroxymethylbilane Synthase (HMBS)
Cat#:TP02465应用:Positive Control; Immunogen; SDS-PAGE; WB
Product Name: | HMBS/PBGD Rabbit pAb |
Cat No.: | DPA01553 |
Clonality: | Polyclonal |
Species Reactivity: | Human, Mouse, Rat |
Tested Applications: | WB |
Recommended Dilution: | WB: 1:1000 |
Size: | 30ul 50ul 100uL |
Format: | Liquid |
Source: | Rabbit |
Purification Method: | Affinity Purification |
Isotype: | IgG |
Conjugate: | Un-conjugated |
Storage: | Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide a |
Immunogen: | A synthetic peptide of human HMBS/PBGD |
Calculated Molecular Weight: | 39 kDa |
Observed Molecular Weight: | 39 kDa |
GenBank Accession Number: | P08397 |
Gene ID (NCBI): | 3145 |
Synonyms: | UPS; PBGD; PORC; PBG-D |
Background: | This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008] |
Category: | Primary Ab |